NAGLU Rabbit Monoclonal Antibody

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Catalog Number:MABN87784
Conjugate:Unconjugated
Size:100μL
Concentration:1mg/ml
Host:Rabbit
Isotype:IgG
Clone:Monoclonal
Immunogen:A synthetic peptide of human NAGLU
Reactivity:Human,Mouse,Rat
Applications:WB 1:500-1:2000,IHC 1:500-1:2000,ICC/IF 1:100-1:200,FC 1:20-1:50
Molecular Weight:Calculated MW:82 kDa; Observed MW:82 kDa
Purification:Affinity Purification
Form:Liquid
Synonyms:NAG; CMT2V; MPS3B; UFHSD; MPS-IIIB

Applications

WB 1:500-1:2000,IHC 1:500-1:2000,ICC/IF 1:100-1:200,FC 1:20-1:50

Immunogen

A synthetic peptide of human NAGLU

Target Background

This gene encodes an enzyme that degrades heparan sulfate by hydrolysis of terminal N-acetyl-D-glucosamine residues in N-acetyl-alpha-D-glucosaminides. Defects in this gene are the cause of mucopolysaccharidosis type IIIB (MPS-IIIB), also known as Sanfilippo syndrome B. This disease is characterized by the lysosomal accumulation and urinary excretion of heparan sulfate. [provided by RefSeq, Jul 2008]

Synonyms:NAG; CMT2V; MPS3B; UFHSD; MPS-IIIB

Storage

Store at 4°C short term. Aliquot and store at -20°C for 12 months. Avoid freeze/thaw cycles.

Buffer

Supplied in 50mM Tris-Glycine(pH 7.4), 0.15M NaCl, 40% Glycerol, 0.01% sodium azide and 0.05% BSA. Stable for 12 months from date of receipt.

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