Immunological Sciences

SGSH Rabbit Monoclonal Antibody

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Catalog Number:MABN21245
Conjugate:Unconjugated
Size:100μL
Concentration:1mg/ml
Host:Rabbit
Isotype:IgG,Kappa
Clone:Monoclonal
Immunogen:Recombinant protein of human SGSH
Reactivity:Human
Applications:WB 1:1000-1:5000,IHC 1:100-1:300,ICC/IF 1:100-1:300
Molecular Weight:CalcuLated MW:;Observed MW:55kD
Purification:Protein A
Form:Liquid
Synonyms:SGSH;HSS;N-suLphoglucosamine suLphohydrolase ;SuLfoglucosamine suLfamidase;SuLphamidase;

Applications

WB 1:1000-1:5000,IHC 1:100-1:300,ICC/IF 1:100-1:300

Immunogen

Recombinant protein of human SGSH

Target Background

Cell localization:Lysosome..This gene encodes the enzyme sulfamidase; one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. [provided by RefSeq, Jun 2017]

Synonyms:SGSH;HSS;N-suLphoglucosamine suLphohydrolase ;SuLfoglucosamine suLfamidase;SuLphamidase;

Storage

Store at 4°C short term. Aliquot and store at -20°C for 12 months. Avoid freeze/thaw cycles.

Buffer

PBS, 50% glycerol, 0.05% Proclin 300, 0.05%BSA

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